Management of Dandy-Walker Syndrome in Children

Initial Management at Presentation

• Treat associated hydrocephalus: Surgical intervention cannot reverse neurological deficits due to Dandy-Walker malformations, so the main concern is to evaluate and treat the child for hydrocephalus.

Follow-up

• Initial confirmation of treatment: In the initial postoperative period, patients are followed to ensure appropriate response to the shunt and/or fenestration.
• Document improving state: Examination should evaluate for improvement in the signs and symptoms of elevated ICP.
• Infection postoperatively: Patients should be monitored for infection in the first 3–6 months after surgery.
• Treatment failure: Patients should be monitored periodically to ensure the hydrocephalus does not return.