Tap on and choose 'Add to Home Screen' to create a shortcut app

Tap on and choose 'Add to Home Screen/Install App' to create a shortcut app

Infratentorial Hemangioblastomas in Children Homepage

This page was last updated on June 9th, 2022



Luca Massimi, M.D.

Section Editor

Kristian Aquilina, M.D.

Editor in Chief

Rick Abbott, M.D.


Hemangioblastomas are slow-growing tumors usually located within the posterior cranial fossa or the spinal cord. In children, hemangioblastomas are very rare and are almost exclusively associated with von Hippel-Lindau disease (VHL). Surgery is the main treatment option. Surgical management may be complicated by the typically large tumor size at presentation and/or its inclination to bleed considerably during surgery. Hemangioblastoma-related surgical mortality is quite high when compared with other tumors of the posterior fossa, especially when the brainstem is involved.

Key Points

  • Evaluation: Clinical and radiological assessments should be very accurate because of the high clinical variability of VHL and the possibility of multiple disease sites.
  • Surgery: Timely neurosurgical treatment is advisable because of the location within the posterior fossa and the typically large tumor size. Gross total tumor resection should be attempted whenever possible since it is curative.

Your donations keep us going

The ISPN Guide is free to use, but we rely on donations to fund our ongoing work and to maintain more than a thousand pages of information created to disseminate the most up-to-date knowledge in the field of paediatric neurosurgery.

By making a donation to The ISPN Guide you are also indirectly helping the many thousands of children around the world whose treatment depends on well-informed surgeons.

Please consider making a donation today.

Use the app

The ISPN Guide can be used as a standalone app, both on mobile devices and desktop computers. It’s quick and easy to use.

Fully featured

Free registration grants you full access to The Guide and host of featured designed to help further your own education.

Stay updated

The ISPN Guide continues to expand both in breadth and depth. Join our mailing list to stay up-to-date with our progress.